Педиатрия и терапия

Педиатрия и терапия
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ISSN: 2161-0665


Atypical HUS with Dysphagia and Palatal Palsy Responding to IVIG

Vivek Kumar *,Kiran Sodhi ,Madhuri Kanitkar ,Deepak ,Anupama ,Ajay Bajpai ,Shonenedra

D negative/Atypical HUS (Hemolytic Uremic Syndrome) is a difficult condition to diagnose and treat. It has been shown to be a disease of complement dysregulation. Treatment is difficult and revolves around plasma exchange. We report one case of an Atypical HUS in a toddler girl who developed multi organ dysfunction associated with never reported dysphagia and palatal paralysis which responded to IVIG (Intravenous Immunoglobulin) given over five days